Pheochromocytoma continues to be a rare tumour in children. It can be missed if a high index of suspicion is not retained in unusually presenting cases. Early diagnosis, accurate localisation of the tumour. careful pre- and intra-operative management are all key to a successful outcome. A l2-year-old boy reported to the Korle-Bu Teaching Hospital in Accra with unusual symptoms. A definitive diagnosis was delayed. His course and outcome 'Ire described with an emphasis on the maintenance of a high degree of suspicion of the diagnosis of phaechromocytoma in children of all ages.