A Rare Paediatric Brain Tumour: Ependymoblastoma -- Case Report and Challenges of Treatment
Authors:
MORGAN Eghosa
Publication Type: Journal article
Journal: Journal Of Clinical And Applied Neurosciences
ISSN Number:
0
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Abstract
Ependymoblastoma is a rare primary malignant brain tumour seen mainly in early childhood. It is embryonal in origin and characterised by uniform neuroepithelial cells with distinctive rosettes and numerous mitotic figures. In this article, we report the case of a 3-year old girl who presented with weakness of the right upper and lower limbs, symptoms and signs of intracranial hypertension and was diagnosed to have ependymoblastoma with characteristic findings on magnetic resonance imaging (MRI). The MRI showed a huge left fronto-parietal heterogeneous mass with ventricular involvement and extension to the contralateral frontal lobe. Histological examination confirmed ependymoblastoma. She had a near total resection via left fronto- parietal craniotomy and subsequently, worked up and had craniospinal radiotherapy and chemotherapy